Dermatofibrosarcoma protuberans, version 1.2014 Review uri icon

Overview

MeSH Major

  • Dermatofibrosarcoma
  • Diagnosis, Differential
  • Neoplasm Recurrence, Local
  • Skin Neoplasms

abstract

  • Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue tumor characterized by a relatively high risk of local recurrence and low risk of metastasis. The NCCN Guidelines for DFSP provide multidisciplinary recommendations on the management of patients with this rare disease. These NCCN Guidelines Insights highlight the addition of the Principles of Pathology section, which provides recommendations on the pathologic assessment of DFSP. Because DFSP can mimic other lesions, immunohistochemical studies are often required to establish diagnosis. Cytogenetic testing for the characteristic translocation t(17;22)(q22;q13) can also be valuable in the differential diagnosis of DFSP with other histologically similar tumors.

authors

publication date

  • June 2014

Research

keywords

  • Review

Identity

Language

  • eng

PubMed ID

  • 24925197

Additional Document Info

start page

  • 863

end page

  • 8

volume

  • 12

number

  • 6