Is Hughes-Stovin syndrome Behçet's disease? Article Report uri icon

Overview

MeSH Major

  • Angioplasty, Balloon
  • Arterial Occlusive Diseases
  • Femoral Artery
  • Iliac Artery
  • Popliteal Artery
  • Tibial Arteries

abstract

  • Hughes-Stovin syndrome (HSS) is a rare clinical disorder which has been described as the presence of pulmonary artery aneurysm in the setting of systemic thrombosis. The term "Incomplete Behçet's Disease" has also been used to describe this syndrome due to the clinical and histopathological similarities between Behçet's disease and HSS. Indeed, pulmonary involvement can be indistinguishable between these two conditions of unknown pathophysiology. We describe an HSS patient who presented with a recurrent pulmonary artery aneurysm, review the clinical and pathological manifestations of HSS, discuss its similarities to Behçet's disease, and finally make the argument that HSS is in fact Behçet's disease. © Copyright Clinical and Experimental Rheumatology 2004.

publication date

  • October 25, 2004

Research

keywords

  • Report

Identity

PubMed ID

  • 15515789

Additional Document Info

start page

  • S64

end page

  • S68

volume

  • 22

number

  • 4 SUPPL. 24