Adult-onset asthma and periocular xanthogranulomas in a patient with lymphoplasmacytic sclerosing pancreatitis Academic Article uri icon


MeSH Major

  • Asthma
  • Granuloma, Plasma Cell
  • Orbital Diseases
  • Pancreatitis
  • Xanthomatosis


  • The clinical syndrome of adult-onset asthma and periocular xanthogranulomas represents a rare systemic autoimmune disorder that has not been previously associated with autoimmune pancreatitis. Herein, we describe the case report of a 61-year-old man with the unique clinical association of adult-onset asthma, atopy, and periocular xanthogranulomas, who had previously been diagnosed with lymphoplasmacytic sclerosing pancreatitis. We have previously reported the case of a patient with lymphoplasmacytic sclerosing pancreatitis that developed postoperative inflammatory pseudotumor of the orbit. These unique, extrapancreatic, ocular manifestations of this disease add to the published observations that it is a systemic disorder with the potential for multiorgan involvement that may have a spectrum of clinical manifestations that includes adult-onset asthma and periocular xanthogranulomas.

publication date

  • January 2007



  • Academic Article



  • eng

Digital Object Identifier (DOI)

  • 10.1097/01.mpa.0000236737.84982.45

PubMed ID

  • 17198199

Additional Document Info

start page

  • 157

end page

  • 60


  • 34


  • 1