Pulmonary dysfunction in adults with nephropathic cystinosis Academic Article Article uri icon

Overview

MeSH Major

  • Adenocarcinoma
  • Algorithms
  • Biomarkers, Tumor
  • Carcinoma, Squamous Cell
  • Immunohistochemistry
  • Lung Neoplasms

abstract

  • The distal myopathy characteristic of nephropathic cystinosis results in an extraparenchymal pattern of restrictive lung disease in adults who have not received long-term cystine depletion. Whether or not oral cysteamine therapy can prevent this complication remains to be determined.

publication date

  • January 2001

Research

keywords

  • Academic Article

Identity

Digital Object Identifier (DOI)

  • 10.1378/chest.119.2.394

PubMed ID

  • 11171714

Additional Document Info

start page

  • 394

end page

  • 401

volume

  • 119

number

  • 2