Malignant endovascular papillary angioendothelioma (Dabska tumor) arising within a deep intramuscular hemangioma Review uri icon

Overview

MeSH Major

  • Hemangioendothelioma
  • Hemangioma, Cavernous
  • Muscle Neoplasms
  • Neoplasms, Second Primary
  • Vascular Neoplasms

abstract

  • We report a rare malignant endovascular papillary angioendothelioma (Dabska tumor) arising within the deep periosteal soft tissue of the ulna of an 8-year-old girl. To our knowledge, this is the first report of a Dabska tumor of deep soft tissue that did not extend down from the dermis. This Dabska tumor appears to be a focal change within a larger, well-defined, cavernous hemangioma of deep muscle. We suggest that this represents secondary neoplastic progression of an existing benign lesion, a common phenomenon among vascular tumors. A review of the family of "hobnailed" endothelial cell lesions to which Dabska tumor belongs is presented.

publication date

  • September 1997

Research

keywords

  • Review

Identity

Language

  • eng

PubMed ID

  • 9302935

Additional Document Info

start page

  • 992

end page

  • 5

volume

  • 121

number

  • 9