Primary type V hyperlipoproteinemia in childhood Academic Article Article uri icon

Overview

MeSH Major

  • Lipoproteins, HDL

abstract

  • Metabolic studies of a 9-year-old girl with primary type V hyperlipoproteinemia demonstrated normal glucose tolerance, plasma insulin and glucagon responses to stimuli, and serum uric acid level. Fasting plasma triglyceride levels rapidly increased when the patient received a diet containing 40% of the total calories as fat and rapidly decreased on a 10% fat diet. Hepatic and nonhepatic lipase activities in postheparin plasma were normal, thus excluding type I hyperlipoproteinemia. Because of the potential complication of acute pancreatitis in this disorder, early diagnosis and prompt institution of diet therapy is important.

publication date

  • December 1977

Research

keywords

  • Academic Article

Identity

Digital Object Identifier (DOI)

  • 10.1001/jama.238.23.2518

PubMed ID

  • 578887

Additional Document Info

start page

  • 2518

end page

  • 20

volume

  • 238

number

  • 23